Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report

Syed Althaf Ali; Syeda Naziya Parveen; Anand Abkari; G. S. N. Murthy; B. Ravindra Prakash

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Case Report

J Med Allied Sci. 2015; 5(1): 10-13

Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report

Syed Althaf Ali, Syeda Naziya Parveen, Anand Abkari, G. S. N. Murthy, B. Ravindra Prakash.

Abstract
Heterotaxy syndrome is a rare embryological disorder comprising of polysplenia, partial agenesis of dorsal pancreas, malrotation of gut, cardiac and vascular anomalies resulting from failure of development of the usual leftright asymmetry of organs. We report a rare case of heterotaxy syndrome with polysplenia, partial agenesis of dorsal pancreas and malrotation of gut in a 28 year female presenting with subacute intestinal obstruction along with imaging illustrations, brief discussion and thorough review of literature.

Key words: Heterotaxy, Polysplenia, Dorsal pancreatic agenesis, Malrotation of gut, Embryogenesis

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How to Cite this Article

Pubmed Style

Syed Althaf Ali, Syeda Naziya Parveen, Anand Abkari, G. S. N. Murthy, B. Ravindra Prakash. Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report. J Med Allied Sci. 2015; 5(1): 10-13.

Web Style

Syed Althaf Ali, Syeda Naziya Parveen, Anand Abkari, G. S. N. Murthy, B. Ravindra Prakash. Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report. https://jmas.in/?mno=211836 [Access: January 12, 2023].

AMA (American Medical Association) Style

Syed Althaf Ali, Syeda Naziya Parveen, Anand Abkari, G. S. N. Murthy, B. Ravindra Prakash. Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report. J Med Allied Sci. 2015; 5(1): 10-13.

Vancouver/ICMJE Style

Harvard Style

Syed Althaf Ali, Syeda Naziya Parveen, Anand Abkari, G. S. N. Murthy, B. Ravindra Prakash (2015) Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report. J Med Allied Sci, 5 (1), 10-13.

Turabian Style

Syed Althaf Ali, Syeda Naziya Parveen, Anand Abkari, G. S. N. Murthy, B. Ravindra Prakash. 2015. Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report. Journal of Medical and Allied Sciences, 5 (1), 10-13.

Chicago Style

Syed Althaf Ali, Syeda Naziya Parveen, Anand Abkari, G. S. N. Murthy, B. Ravindra Prakash. "Heterotaxy syndrome with associated agenesis of dorsal pancreas and polysplenia: A case report." Journal of Medical and Allied Sciences 5 (2015), 10-13.

MLA (The Modern Language Association) Style

APA (American Psychological Association) Style

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