E-ISSN 2231-170X | ISSN 2231-1696
 

Case Report 


Report of two rare cases of Kindler's syndrome in siblings

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty.

Abstract
Kindler’s syndrome is a rare autosomal recessive disorder. It is characterized by trauma-induced blistering, photosensitivity, poikiloderma and mucosal inflammation. It occurs due to mutation on chromosome 20p. This report describes two siblings with history of blistering and photosensitivity in childhood and later developed poikiloderma with histopathology of effected skin showing features of poikiloderma.

Key words: Kindler's syndrome, Photosensitivity, Poikiloderma


 
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How to Cite this Article
Pubmed Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty. Report of two rare cases of Kindler's syndrome in siblings. J Med Allied Sci. 2017; 7(2): 118-121. doi:10.5455/jmas.260417


Web Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty. Report of two rare cases of Kindler's syndrome in siblings. https://jmas.in/?mno=260417 [Access: December 05, 2023]. doi:10.5455/jmas.260417


AMA (American Medical Association) Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty. Report of two rare cases of Kindler's syndrome in siblings. J Med Allied Sci. 2017; 7(2): 118-121. doi:10.5455/jmas.260417



Vancouver/ICMJE Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty. Report of two rare cases of Kindler's syndrome in siblings. J Med Allied Sci. (2017), [cited December 05, 2023]; 7(2): 118-121. doi:10.5455/jmas.260417



Harvard Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty (2017) Report of two rare cases of Kindler's syndrome in siblings. J Med Allied Sci, 7 (2), 118-121. doi:10.5455/jmas.260417



Turabian Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty. 2017. Report of two rare cases of Kindler's syndrome in siblings. Journal of Medical and Allied Sciences, 7 (2), 118-121. doi:10.5455/jmas.260417



Chicago Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty. "Report of two rare cases of Kindler's syndrome in siblings." Journal of Medical and Allied Sciences 7 (2017), 118-121. doi:10.5455/jmas.260417



MLA (The Modern Language Association) Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty. "Report of two rare cases of Kindler's syndrome in siblings." Journal of Medical and Allied Sciences 7.2 (2017), 118-121. Print. doi:10.5455/jmas.260417



APA (American Psychological Association) Style

Neha Chowdary Koganti, Nayeem Sadath Haneef, Fatima Razvi, B. Y. Praveen Kumar, Nikhat Fatima, Mohammed Altamash Zubair, Debasmita Chakraborty (2017) Report of two rare cases of Kindler's syndrome in siblings. Journal of Medical and Allied Sciences, 7 (2), 118-121. doi:10.5455/jmas.260417