E-ISSN 2231-170X | ISSN 2231-1696
 

Case Report
Online Published: 29 Jan 2017
 


Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida.


Cited By: 1

Abstract
Pleuropulmonary blastoma (PPB) is a rare aggressive malignant tumor of infancy and early childhood accounting for 0.25-0.5% of primary lung tumors. PPB is a dysontogenic tumor composed of immature malignant epithelial and/or mesenchymal tissues whose features may resemble early embryological lung tissues. It is the pulmonary analog of other tumors of childhood including Wilms' tumor, neuroblastoma, hepatoblastoma, pancreatoblastoma and retinoblastoma. Morphologically, PPB has three types (I, II, and III). A fourth type (Ir) was added in 2006 by PPB registry. Type II and III are very aggressive malignancies with metastatic potential. Bilateral PPB is very rare. To the best of our knowledge, only two cases of bilateral PPB have been reported. No cases of bilateral PPB have been reported from India. Herein, we are reporting a case of bilateral PPB (type II) in a 2-year-old girl who presented with cough, dyspnea and mild fever for past 4 months. She died few days after admission.

Key words: Bilateral pleuropulmonary blastoma, Bronchogenic cyst, Congenital pulmonary airway malformations, Dysontogenic tumor, PPB registry, Primitive neuroectodermal tumors


 
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How to Cite this Article
Pubmed Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci. 2017; 7(1): 67-71. doi:10.5455/jmas.252500


Web Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. https://jmas.in/?mno=252500 [Access: September 12, 2024]. doi:10.5455/jmas.252500


AMA (American Medical Association) Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci. 2017; 7(1): 67-71. doi:10.5455/jmas.252500



Vancouver/ICMJE Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci. (2017), [cited September 12, 2024]; 7(1): 67-71. doi:10.5455/jmas.252500



Harvard Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida (2017) Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. J Med Allied Sci, 7 (1), 67-71. doi:10.5455/jmas.252500



Turabian Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida. 2017. Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. Journal of Medical and Allied Sciences, 7 (1), 67-71. doi:10.5455/jmas.252500



Chicago Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida. "Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature." Journal of Medical and Allied Sciences 7 (2017), 67-71. doi:10.5455/jmas.252500



MLA (The Modern Language Association) Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida. "Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature." Journal of Medical and Allied Sciences 7.1 (2017), 67-71. Print. doi:10.5455/jmas.252500



APA (American Psychological Association) Style

Pradosh Kumar Sarangi, H. S. Sagar, Sanjay Kumar Nahak, Jayashree Mohanty, Sasmita Parida (2017) Bilateral pleuropulmonary blastoma (PPB) in a 2-year-old girl: A case report with review of literature. Journal of Medical and Allied Sciences, 7 (1), 67-71. doi:10.5455/jmas.252500